Background :Calcifying odontogenic cyst (COC) is an uncommon developmental odontogenic cyst first described by Gorlin in 1962. It is named cystic calcifying odontogenic tumor in new classification. It is considered as extremely rare and accounts for only 1% of jaw cysts reported. It is unusually seen associated to odontoma.

  Case Report:The case was A 15 year-old male patient  with the chief complaints of  painless swelling in the right side of anterior part  of his maxilla. Radiographic pattern was radiolucent with radioopacitis foci . In histopathological view, epithelium of odontogenic cyst with ghost cells and complex odontoma were seen. Treatment was done by enucleation,in six mounths follow up there was not any reccurence. 

  Conclusion : Clinical and radiographical features of odontogenic lesions were non-specific. Always we must careful that the type of lesion associated to Gorlin cyst appoints the clinical behavior, method of treatment and prognosis of combined lesion.

  Keywords: Calcifying odontogenic cyst , Ghost cell, Gorlin cyst, Odontoma